Verified
Z00.129 - Encounter for routine child health examination without abnormal findings
A regular check-up or wellness visit for a child where everything was found to be normal.

Clinical Definition
Cystic fibrosis with acute exacerbation is a genetic disorder characterized by thick, sticky mucus affecting multiple organ systems, specifically during a period of worsening respiratory symptoms requiring intervention.
Documentation Requirements
Must document genetic confirmation of cystic fibrosis (CF)
Specify "acute exacerbation" or "acute worsening"
Document at least one of:
Increased cough
Increased sputum production
Change in sputum characteristics
Decreased lung function from baseline
New or increased chest infiltrates
Include severity indicators
Document treatment changes (e.g., new antibiotics, increased airway clearance)
Specify any additional organ systems affected
Common Synonyms
"CF flare-up"
"CF lung infection"
"Getting worse/breaking through"
"Breathing problems getting worse"
"Need for rescue antibiotics"
Coding Conflicts
Excludes1:
Mucoviscidosis in other organs
Initial diagnosis of cystic fibrosis
Cystic fibrosis carrier state
Must not be coded with:
Bronchiectasis
Other chronic pulmonary conditions
Scribing.io Automation
The AI scribe automatically identifies:
Keywords indicating acute exacerbation ("worsening," "flare," "exacerbation")
Changes in respiratory symptoms from baseline
Documentation of new treatments or interventions
Links to previous CF diagnosis
Captures pulmonary function test results
Flags any missing documentation elements needed for coding validation

